Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001783262 | SCV003494474 | pathogenic | Fanconi anemia complementation group E | 2023-08-25 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Ser112Valfs*14) in the FANCE gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in FANCE are known to be pathogenic (PMID: 11001585, 17924555). This variant is present in population databases (no rsID available, gnomAD 0.0009%). For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 1322887). This premature translational stop signal has been observed in individual(s) with Fanconi anemia (PMID: 32947577). |
Baylor Genetics | RCV001783262 | SCV004196804 | pathogenic | Fanconi anemia complementation group E | 2023-06-23 | criteria provided, single submitter | clinical testing |