Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002917255 | SCV003249021 | pathogenic | not provided | 2022-04-25 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Asp593Leufs*2) in the RINT1 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in RINT1 are known to be pathogenic (PMID: 31204009). This variant is present in population databases (no rsID available, gnomAD 0.0009%). This variant has not been reported in the literature in individuals affected with RINT1-related conditions. For these reasons, this variant has been classified as Pathogenic. |
Ambry Genetics | RCV004066062 | SCV003855070 | uncertain significance | not specified | 2022-11-04 | criteria provided, single submitter | clinical testing | The c.1773_1776dupCTTT variant, located in coding exon 12 of the RINT1 gene, results from a duplication of CTTT at nucleotide position 1773, causing a translational frameshift with a predicted alternate stop codon (p.D593Lfs*2). This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. The evidence for this gene-disease relationship is limited; therefore, the clinical significance of this alteration is unclear. |