Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Dept. |
RCV000043650 | SCV005081817 | uncertain significance | Cataract 14 multiple types | 2023-01-21 | criteria provided, single submitter | curation | Variant identified and curated during a GJA3 specific review of the literature in relation to pediatric or congenital cataract. ACMG-AMP criteria applied: PM2(Supporting), PP1, PP3. Original variant report: PMID:22550389. The cataract phenotype reported for this variant is: Nuclear. Gene review and curation guidelines are outlined in: https://doi.org/10.1080/17469899.2023.2160320 |
OMIM | RCV000043650 | SCV000071672 | pathogenic | Cataract 14 multiple types | 2012-01-01 | no assertion criteria provided | literature only | |
Prevention |
RCV004755757 | SCV005360153 | likely pathogenic | GJA3-related disorder | 2024-06-27 | no assertion criteria provided | clinical testing | The GJA3 c.616T>A variant is predicted to result in the amino acid substitution p.Phe206Ile. This variant has been reported to segregate with disease in a three-generation kindred with congenital cataracts (Wang et al 2012. PubMed ID: 22550389). This variant has not been reported in a large population database, indicating this variant is rare. This variant is interpreted as likely pathogenic. |