Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002958596 | SCV003277217 | uncertain significance | Cataract 14 multiple types | 2023-01-01 | criteria provided, single submitter | clinical testing | Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt GJA3 protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has not been reported in the literature in individuals affected with GJA3-related conditions. This sequence change replaces leucine, which is neutral and non-polar, with arginine, which is basic and polar, at codon 302 of the GJA3 protein (p.Leu302Arg). This variant is present in population databases (rs758716786, gnomAD 0.05%). |
Prevention |
RCV003409988 | SCV004116002 | uncertain significance | GJA3-related disorder | 2023-01-19 | criteria provided, single submitter | clinical testing | The GJA3 c.905T>G variant is predicted to result in the amino acid substitution p.Leu302Arg. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.036% of alleles in individuals of African descent in gnomAD (http://gnomad.broadinstitute.org/variant/13-20716523-A-C). Although we suspect that this variant may be benign, at this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |
Ambry Genetics | RCV004068065 | SCV004876954 | uncertain significance | Inborn genetic diseases | 2023-10-05 | criteria provided, single submitter | clinical testing | The c.905T>G (p.L302R) alteration is located in exon 2 (coding exon 1) of the GJA3 gene. This alteration results from a T to G substitution at nucleotide position 905, causing the leucine (L) at amino acid position 302 to be replaced by an arginine (R). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |