Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV003228577 | SCV003925127 | uncertain significance | Inherited obesity | 2022-05-17 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004747276 | SCV005358207 | uncertain significance | NR0B2-related disorder | 2024-08-19 | no assertion criteria provided | clinical testing | The NR0B2 c.637C>T variant is predicted to result in the amino acid substitution p.Arg213Cys. This variant was reported in an individual with mild obesity (Nishigori et al. 2001. PubMed ID: 11136233) and in vitro functional studies show this variant impacts protein function (Nishigori et al. 2001. PubMed ID: 11136233; Boulias et al. 2004. PubMed ID: 15550569). This variant is reported in 0.055% of alleles in individuals of East Asian descent in gnomAD. Although we suspect that this variant may be pathogenic, at this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |