Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003502497 | SCV004313909 | uncertain significance | Erythrocytosis, familial, 3 | 2023-05-30 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has not been reported in the literature in individuals affected with EGLN1-related conditions. This variant is not present in population databases (gnomAD no frequency). This variant, c.668_673dup, results in the insertion of 2 amino acid(s) of the EGLN1 protein (p.Gly223_Asp224dup), but otherwise preserves the integrity of the reading frame. |