Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001067279 | SCV001232332 | likely benign | Singleton-Merten syndrome 1; Aicardi-Goutieres syndrome 7 | 2023-12-19 | criteria provided, single submitter | clinical testing | |
Ce |
RCV003438658 | SCV004147076 | uncertain significance | not provided | 2023-03-01 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004629441 | SCV005123648 | uncertain significance | Inborn genetic diseases | 2024-04-26 | criteria provided, single submitter | clinical testing | The c.2642T>C (p.I881T) alteration is located in exon 14 (coding exon 14) of the IFIH1 gene. This alteration results from a T to C substitution at nucleotide position 2642, causing the isoleucine (I) at amino acid position 881 to be replaced by a threonine (T). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |