Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV003232621 | SCV002758033 | likely pathogenic | Sotos syndrome | 2022-12-05 | criteria provided, single submitter | clinical testing | The variant c.2889_2890del (p.(His963Glnfs*16)) in exon 5 of the NSD1 gene is not found in the gnomAD database and it creates a frame shift starting at codon His963. The new reading frame ends in a STOP codon at position 16. ACMG criteria used for classification: PVS1, PM2. |