Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV003231250 | SCV000194184 | pathogenic | Sotos syndrome | 2013-02-08 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002336291 | SCV002639625 | uncertain significance | Inborn genetic diseases | 2020-05-21 | criteria provided, single submitter | clinical testing | The p.S1636F variant (also known as c.4907C>T), located in coding exon 12 of the NSD1 gene, results from a C to T substitution at nucleotide position 4907. The serine at codon 1636 is replaced by phenylalanine, an amino acid with highly dissimilar properties. This amino acid position is well conserved in available vertebrate species. In addition, this alteration is predicted to be deleterious by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |