Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Department of Medical Genetics, |
RCV003459832 | SCV003935263 | pathogenic | Sotos syndrome | criteria provided, single submitter | clinical testing | The p.Cys1643Ser variant on the NSD1 is classified as Likely pathogenic according to the ACMG guidelines. It complies with the PP3, PM1, and PM2 criteria. It was detected via Clinical Exome Sequencing in male patient with typical Sotos syndrome phenotype. Therefore, it is associated to the phenotype of our pateint and meets our criteria to be classified as pathogenic. |