Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004719711 | SCV005325650 | likely pathogenic | not provided | 2023-12-10 | criteria provided, single submitter | clinical testing | In silico analysis supports that this variant does not alter splicing; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 32169219, 24965254, 27264804, 18156157, 31395865, 14727139) |
Juno Genomics, |
RCV004796040 | SCV005418572 | likely pathogenic | Acheiropodia; Laurin-Sandrow syndrome; Polydactyly of a triphalangeal thumb; Syndactyly type 4; Tibia, hypoplasia or aplasia of, with polydactyly; Triphalangeal thumb-polysyndactyly syndrome | criteria provided, single submitter | clinical testing | PM2_Supporting+PS4_Supporting+PP1+PP4+PM1 | |
OMIM | RCV003991466 | SCV004801323 | pathogenic | Tibia, hypoplasia or aplasia of, with polydactyly | 2014-08-01 | no assertion criteria provided | literature only |