Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV003314416 | SCV004013742 | likely pathogenic | Focal segmental glomerulosclerosis 5 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. Missense changes are a common disease-causing mechanism. In silico tool predictions suggest damaging effect of the variant on gene or gene product (REVEL: 0.71; 3Cnet: 0.93). Same nucleotide change resulting in same amino acid change has been previously reported to be associated with INF2 related disorder (PMID: 21866090). A different missense change at the same codon (p.Asn202Ser) has been reported to be associated with INF2 -related disorder (ClinVar ID: VCV001697256 / PMID: 21415313). Therefore, this variant is classified as Likely pathogenic according to the recommendation of ACMG/AMP guideline. |