Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clinical Genomics Laboratory, |
RCV005055005 | SCV005688763 | uncertain significance | Tatton-Brown-Rahman overgrowth syndrome | 2023-08-09 | criteria provided, single submitter | clinical testing | The DNMT3A c.364G>C (p.Ala122Pro) variant has not been reported in the medical literature to our knowledge. This variant is absent from the general population (gnomAD v.2.1.1), indicating it is not a common variant. Computational predictors are uncertain/conflicting as to the impact of this variant on DNTM3A protein function. Due to limited information, and based on ACMG/AMP guidelines for variant interpretation (Richards S et al., PMID: 25741868), the clinical significance of this variant is uncertain at this time. |