Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001245827 | SCV001419145 | uncertain significance | Fanconi anemia | 2023-06-16 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine, which is basic and polar, with glycine, which is neutral and non-polar, at codon 122 of the FANCF protein (p.Arg122Gly). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt FANCF protein function. ClinVar contains an entry for this variant (Variation ID: 970279). This variant has not been reported in the literature in individuals affected with FANCF-related conditions. This variant is present in population databases (rs759470099, gnomAD 0.003%). |
Fulgent Genetics, |
RCV002484370 | SCV002776153 | uncertain significance | Fanconi anemia complementation group F | 2021-12-26 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004619586 | SCV005113438 | uncertain significance | Inborn genetic diseases | 2024-03-29 | criteria provided, single submitter | clinical testing | The c.364C>G (p.R122G) alteration is located in exon 1 (coding exon 1) of the FANCF gene. This alteration results from a C to G substitution at nucleotide position 364, causing the arginine (R) at amino acid position 122 to be replaced by a glycine (G). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |