Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV001817941 | SCV002067450 | uncertain significance | not specified | 2020-03-13 | criteria provided, single submitter | clinical testing | DNA sequence analysis of the FANCF gene demonstrated a 3 base pair duplication in exon 1, c.632_634dup. This in-frame deletion is predicted to result in the duplication of 1 amino acid residue, p.Gln211dup. This sequence change has been described in the gnomAD database in 2 individuals (dbSNP rs748880303). The p.Gln211dup change is located in a domain of the FANCF protein that is not known to be functional. This sequence change has not been previously reported in patients with FANCF-related disorders; however, frameshift deletions in FANCF have been reported in patients with Fanconi anemia (PMIDs: 27714961, 31288759). The functional significance of this sequence change is not known at present and its contribution to a disease phenotype cannot definitively be determined. |