Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001712193 | SCV000513249 | likely benign | not provided | 2021-06-25 | criteria provided, single submitter | clinical testing | |
Genetic Services Laboratory, |
RCV000417949 | SCV000595132 | benign | not specified | 2017-07-26 | criteria provided, single submitter | clinical testing | |
Athena Diagnostics | RCV000417949 | SCV001880067 | benign | not specified | 2021-04-06 | criteria provided, single submitter | clinical testing | |
Clinical Genomics, |
RCV002328914 | SCV002601638 | likely benign | Maturity onset diabetes mellitus in young | criteria provided, single submitter | research | Mutations in HNF1A gene can predispose to MODY3. It is associated with both micro and macrovascular complications of diabetes, especially cardiovascular complications. Associated with glucosuria. May respond well to sulfonylureas. However, more evidence is required to confer the association of this particular variant rs112986697 with MODY3. | |
Ambry Genetics | RCV002328914 | SCV002736835 | uncertain significance | Maturity onset diabetes mellitus in young | 2015-09-27 | criteria provided, single submitter | clinical testing | The c.*5G>A variant is located in the 3' untranslated region (3’ UTR) of the HNF1A gene. This variant results from a G to A substitution five bases downstream of the last translated codon. This variant was previously reported in the SNPDatabase as rs112986697. Based on data from the 1000 Genomes Project, the A allele has an overall frequency of approximately 0.14% (3/2098) total alleles studied. The highest observed frequency was 0.86% (1/116) Mexican-American alleles. Based on data from the NHLBI Exome Sequencing Project (ESP), the A allele has an overall frequency of approximately 0.28% (37/13006) total alleles studied, having been observed in 0.84% (37/4406) African American alleles. This nucleotide position is highly conserved in available vertebrate species. Since supporting evidence is limited at this time, the clinical significance of this variant remains unclear. |