Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Medical Genetics, |
RCV001730096 | SCV001976926 | uncertain significance | Trigonocephaly 1 | 2021-10-06 | criteria provided, single submitter | clinical testing | PM2, PP2, PP3 |
3billion | RCV001779338 | SCV002014724 | uncertain significance | Osteoglophonic dysplasia | 2021-10-25 | criteria provided, single submitter | clinical testing | This variant is not observed in the gnomAD v2.1.1 dataset (PM2). In silico tool predictions suggest damaging effect of the variant on gene or gene product (3Cnet: 0.905, PP3). Therefore, this variant is classified as uncertain significance according to the recommendation of ACMG/AMP guideline. |