Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001774037 | SCV001994514 | uncertain significance | not provided | 2023-04-14 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis, which includes protein predictors and evolutionary conservation, supports a deleterious effect; Has not been previously published as a pathogenic or benign germline variant to our knowledge |
Illumina Laboratory Services, |
RCV001796998 | SCV002038570 | uncertain significance | FGFR1-related craniosynostosis syndrome | 2021-06-18 | criteria provided, single submitter | clinical testing | The FGFR1 c.1982G>A (p.Arg661Gln) variant is a missense variant. A literature search was performed for the gene, cDNA change, and amino acid change. No informative publications were found based on this search. This variant is not found in version 2.1.1 or version 3.1.1 of the Genome Aggregation Database despite its location in a region of good sequencing coverage, which suggests the variant is rare. Multiple in-silico variant effect predictor algorithms indicate a deleterious impact for this variant, though these predictions have not been experimentally confirmed. Based on the available evidence, the p.Arg661Gln variant is classified as a variant of uncertain significance for FGFR1-related craniosynostosis syndrome. |
Reproductive Endocrine Unit, |
RCV003234584 | SCV003932574 | likely pathogenic | Hypogonadotropic hypogonadism 2 with or without anosmia | 2023-05-04 | criteria provided, single submitter | research |