Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV003442898 | SCV001906474 | likely pathogenic | not provided | 2021-08-27 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (Lek et al., 2016); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function |
OMIM | RCV001779314 | SCV002016206 | pathogenic | Neurodevelopmental disorder with hearing loss and spasticity | 2023-04-19 | no assertion criteria provided | literature only |