Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV001336087 | SCV001529383 | uncertain significance | Intellectual disability, autosomal recessive 57 | 2018-02-06 | criteria provided, single submitter | clinical testing | This variant was determined to be of uncertain significance according to ACMG Guidelines, 2015 [PMID:25741868]. |
Ambry Genetics | RCV002546761 | SCV003731176 | uncertain significance | Inborn genetic diseases | 2021-01-08 | criteria provided, single submitter | clinical testing | The c.1366A>G (p.K456E) alteration is located in exon 8 (coding exon 7) of the MBOAT7 gene. This alteration results from a A to G substitution at nucleotide position 1366, causing the lysine (K) at amino acid position 456 to be replaced by a glutamic acid (E). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |