Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mendelics | RCV000018094 | SCV001142168 | uncertain significance | Spinocerebellar ataxia type 23 | 2023-09-29 | criteria provided, single submitter | clinical testing | |
Institute of Medical Genetics and Applied Genomics, |
RCV001268483 | SCV001447446 | pathogenic | not provided | 2020-10-23 | criteria provided, single submitter | clinical testing | |
Ce |
RCV001268483 | SCV002064033 | likely pathogenic | not provided | 2021-10-01 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001268483 | SCV002584237 | uncertain significance | not provided | 2023-09-21 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant does not alter protein structure/function; This variant is associated with the following publications: (PMID: 31589614, 21035104) |
Labcorp Genetics |
RCV001268483 | SCV003262120 | pathogenic | not provided | 2022-07-30 | criteria provided, single submitter | clinical testing | This missense change has been observed in individual(s) with clinical features of spinocerebellar ataxia (PMID: 21035104, 22287014, 23355175). It has also been observed to segregate with disease in related individuals. This variant is present in population databases (rs267606941, gnomAD 0.01%). This sequence change replaces arginine, which is basic and polar, with serine, which is neutral and polar, at codon 138 of the PDYN protein (p.Arg138Ser). ClinVar contains an entry for this variant (Variation ID: 18458). For these reasons, this variant has been classified as Pathogenic. Studies have shown that this missense change alters PDYN gene expression (PMID: 21035104). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0"). |
Human Genetics Bochum, |
RCV000018094 | SCV004042773 | likely pathogenic | Spinocerebellar ataxia type 23 | 2023-05-23 | criteria provided, single submitter | clinical testing | ACMG criteria used to clasify this variant: PS4, PS3_MOD, PP1 |
OMIM | RCV000018094 | SCV000038373 | pathogenic | Spinocerebellar ataxia type 23 | 2010-11-12 | no assertion criteria provided | literature only |