Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002508734 | SCV002818058 | uncertain significance | not provided | 2022-12-22 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis is inconclusive as to whether the variant alters gene splicing. In the absence of RNA/functional studies, the actual effect of this sequence change is unknown.; This variant is associated with the following publications: (PMID: 23871674, 31402444, 21606396) |
Color Diagnostics, |
RCV003533276 | SCV004363107 | uncertain significance | Cardiomyopathy | 2024-05-03 | criteria provided, single submitter | clinical testing | This variant causes an A to G nucleotide substitution at the +3 position of intron 7 of the DSC2 gene. To our knowledge, functional studies have not been reported for this variant. This variant has been reported in at least 1 individual affected with arrhythmogenic right ventricular cardiomyopathy/dysplasia (PMID: 21606396). This variant has been identified in 3/282790 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
All of Us Research Program, |
RCV004808357 | SCV005427487 | uncertain significance | Familial isolated arrhythmogenic right ventricular dysplasia | 2024-05-14 | criteria provided, single submitter | clinical testing | This variant causes an A to G nucleotide substitution at the +3 position of intron 7 of the DSC2 gene. To our knowledge, functional studies have not been reported for this variant. This variant has been reported in at least 1 individual affected with arrhythmogenic right ventricular cardiomyopathy/dysplasia (PMID: 21606396). This variant has been identified in 3/282790 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |