Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory Oncology Unit, |
RCV000766274 | SCV000897759 | uncertain significance | Acute myeloid leukemia | 2018-12-06 | criteria provided, single submitter | research | |
3billion | RCV003152731 | SCV003842087 | uncertain significance | Nephrotic syndrome, type 4 | 2023-02-23 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. In silico tool predictions suggest damaging effect of the variant on gene or gene product (REVEL: 0.56; 3Cnet: 0.76). A different missense change at the same codon (p.Arg463Gln) has been reported to be associated with WT1 related disorder (ClinVar ID: VCV000599100 / PMID: 25145932 / 3billion dataset). However the evidence of pathogenicity is insufficient at this time. Therefore, this variant is classified as VUS according to the recommendation of ACMG/AMP guideline. |