Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001995166 | SCV002249703 | uncertain significance | Drash syndrome; Frasier syndrome; Wilms tumor 1; 11p partial monosomy syndrome | 2023-10-11 | criteria provided, single submitter | clinical testing | This sequence change falls in intron 2 of the WT1 gene. It does not directly change the encoded amino acid sequence of the WT1 protein. This variant is present in population databases (no rsID available, gnomAD 0.006%). This variant has not been reported in the literature in individuals affected with WT1-related conditions. ClinVar contains an entry for this variant (Variation ID: 1470255). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may create or strengthen a splice site. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Fulgent Genetics, |
RCV002492178 | SCV002777731 | uncertain significance | Aniridia 1; Drash syndrome; Frasier syndrome; Meacham syndrome; Mesothelioma, malignant; Nephrotic syndrome, type 4; Wilms tumor 1; 11p partial monosomy syndrome | 2022-03-03 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV003464337 | SCV004206926 | uncertain significance | Drash syndrome | 2024-01-04 | criteria provided, single submitter | clinical testing | |
All of Us Research Program, |
RCV004011015 | SCV004815845 | uncertain significance | Wilms tumor 1 | 2023-12-18 | criteria provided, single submitter | clinical testing | This variant causes a G>A nucleotide substitution at the -14 position of intron 2 of the WT1 gene. Splice site prediction tools are inconclusive regarding the impact of this variant on RNA splicing. To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with WT1-related disorders in the literature. This variant has been identified in 5/258694 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |