Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000703641 | SCV000832550 | uncertain significance | Combined oxidative phosphorylation defect type 27 | 2018-05-02 | criteria provided, single submitter | clinical testing | This sequence change replaces valine with glycine at codon 52 of the CARS2 protein (p.Val52Gly). The valine residue is weakly conserved and there is a moderate physicochemical difference between valine and glycine. While this variant is not present in population databases, the frequency information is unreliable, as metrics indicate poor data quality at this position in the ExAC database. This variant has not been reported in the literature in individuals with CARS2-related disease. Algorithms developed to predict the effect of missense changes on protein structure and function do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Class C0"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
OMIM | RCV000703641 | SCV002106390 | pathogenic | Combined oxidative phosphorylation defect type 27 | 2022-03-17 | no assertion criteria provided | literature only |