Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001213338 | SCV001384964 | uncertain significance | Combined oxidative phosphorylation defect type 27 | 2023-07-06 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is expected to disrupt CARS2 protein function. ClinVar contains an entry for this variant (Variation ID: 943195). This variant has not been reported in the literature in individuals affected with CARS2-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces cysteine, which is neutral and slightly polar, with arginine, which is basic and polar, at codon 290 of the CARS2 protein (p.Cys290Arg). |
Fulgent Genetics, |
RCV001213338 | SCV002812860 | uncertain significance | Combined oxidative phosphorylation defect type 27 | 2021-09-16 | criteria provided, single submitter | clinical testing |