Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000471198 | SCV000551450 | likely pathogenic | Amelocerebrohypohidrotic syndrome | 2018-09-01 | criteria provided, single submitter | clinical testing | In summary, donor and acceptor splice site variants are typically truncating (PMID: 16199547), and truncating variants in ROGDI are known to be pathogenic (PMID: 22424600). However, without additional functional and/or genetic data, this variant has been classified as Likely Pathogenic. This variant has not been reported in the literature in individuals with a ROGDI-related disease. This sequence change affects an acceptor splice site in intron 2 of the ROGDI gene. It is expected to disrupt RNA splicing and likely results in an absent or disrupted protein product. |