Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV005288474 | SCV005956304 | uncertain significance | Inborn genetic diseases | 2025-03-11 | criteria provided, single submitter | clinical testing | The p.P104L variant (also known as c.311C>T), located in coding exon 3 of the USB1 gene, results from a C to T substitution at nucleotide position 311. The proline at codon 104 is replaced by leucine, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |