Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004517665 | SCV005028810 | uncertain significance | not specified | 2023-12-18 | criteria provided, single submitter | clinical testing | The c.139_152dup14 variant, located in coding exon 1 of the GALNT12 gene, results from a duplication of GCTGCCGAGCCGGG at nucleotide position 139, causing a translational frameshift with a predicted alternate stop codon (p.P52Lfs*96). The predicted stop codon occurs in the 5’ end of theGALNT12 gene. Premature termination codons in the 5’ end of a gene have been reported to escape nonsense-mediated mRNAdecay and/or lead to re-initiation (Rivas et al. Science. 2015 May 8;348(6235):666-9; Lindeboom et al. Nat Genet. 2016 Oct;48(10):1112-8; Rhee et al. Sci Rep. 2017 May 10;7(1):1653). The exact functional effect of this alteration is unknown. In addition, the evidence for this gene-disease relationship is limited; therefore, the clinical significance of this alteration is unclear. |