Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV002510758 | SCV002820326 | uncertain significance | Combined oxidative phosphorylation defect type 24 | criteria provided, single submitter | clinical testing | The missense variant p.L34V in NARS2 (NM_024678.6) has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.L34V variant is observed in 5/30,616 (0.0163%) alleles from individuals of South Asian background in gnomAD Exomes and is novel (not in any individuals) in 1000 Genomes. In silico tools predict a damaging effect and the residue is conserved across species. For these reasons, this variant has been classified as Uncertain Significance. |