Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Medical Genetics |
RCV001172268 | SCV001237459 | pathogenic | Bardet-Biedl syndrome | 2020-04-15 | criteria provided, single submitter | clinical testing | absent from gnomAD and 1000genomes, position 339 is buried in the apical domain within the chaperonin type II superfamily topology at a relatively conserved position accepting only hydrophobic residues (mostly Valine, Leucine and Isoleucine). The Grantham distance is as expected high (152) when comparing a Valine (hydrophobic) to an Aspartic acid (Acidic). |