Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002016098 | SCV002305686 | uncertain significance | Familial aplasia of the vermis; Meckel-Gruber syndrome | 2022-02-22 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals affected with TCTN2-related conditions. This sequence change replaces serine, which is neutral and polar, with phenylalanine, which is neutral and non-polar, at codon 112 of the TCTN2 protein (p.Ser112Phe). This variant is not present in population databases (gnomAD no frequency). Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The phenylalanine amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV004970775 | SCV005511823 | uncertain significance | Inborn genetic diseases | 2024-08-12 | criteria provided, single submitter | clinical testing | The c.335C>T (p.S112F) alteration is located in exon 4 (coding exon 4) of the TCTN2 gene. This alteration results from a C to T substitution at nucleotide position 335, causing the serine (S) at amino acid position 112 to be replaced by a phenylalanine (F). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |