Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genomic Medicine Center of Excellence, |
RCV001727916 | SCV005038840 | pathogenic | Biliary, renal, neurologic, and skeletal syndrome | 2024-03-14 | criteria provided, single submitter | clinical testing | |
Gene |
RCV004720929 | SCV005328168 | likely pathogenic | not provided | 2024-03-11 | criteria provided, single submitter | clinical testing | Canonical splice site variant predicted to result in an in-frame loss of the adjacent exon in a gene for which loss of function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 32552793, 31595528, 34177428) |
Genomic Medicine Center of Excellence, |
RCV001844310 | SCV001870538 | pathogenic | Hydrocephalus | 2021-04-29 | no assertion criteria provided | research | |
OMIM | RCV001727916 | SCV001976499 | pathogenic | Biliary, renal, neurologic, and skeletal syndrome | 2021-10-04 | no assertion criteria provided | literature only |