Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001901602 | SCV002173219 | pathogenic | Odonto-onycho-dermal dysplasia; Tooth agenesis, selective, 4 | 2023-06-03 | criteria provided, single submitter | clinical testing | ClinVar contains an entry for this variant (Variation ID: 1404347). For these reasons, this variant has been classified as Pathogenic. This variant has not been reported in the literature in individuals affected with WNT10A-related conditions. This variant is present in population databases (rs781237311, gnomAD 0.001%). This sequence change creates a premature translational stop signal (p.Leu29Tyrfs*34) in the WNT10A gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in WNT10A are known to be pathogenic (PMID: 17847007, 22581971, 25629078). |