Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001036230 | SCV001199582 | uncertain significance | Biotin-responsive basal ganglia disease | 2019-11-18 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has not been reported in the literature in individuals with SLC19A3-related conditions. This variant is not present in population databases (ExAC no frequency). This sequence change results in a frameshift in the SLC19A3 gene (p.Lys495Cysfs*21). While this is not anticipated to result in nonsense mediated decay, it is expected to disrupt the last 2 amino acids of the SLC19A3 protein and extend the protein by an additional 18 amino acids. |