Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Servicio de Genética Del Instituto Nacional de Salud Del Niño, |
RCV004794758 | SCV005414495 | uncertain significance | Smith-Magenis syndrome | 2024-11-18 | criteria provided, single submitter | clinical testing | The variant NM_030665.4:c.5554G>A results in the substitution of alanine with threonine at position 1852 in the protein. Alanine is a small, non-polar amino acid, while threonine contains a hydroxyl group, which could potentially affect the protein's structure or function. Based on PM2 (absence from controls or databases), this variant is classified as uncertain significance |