Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetics and Molecular Pathology, |
RCV003447686 | SCV004175261 | uncertain significance | CFHR5 deficiency | 2022-10-04 | criteria provided, single submitter | clinical testing | The CFHR5 c.1321C>T variant is classified as VUS (PM2) The CFHR5 c.1321C>T variant is a single nucleotide change in exon 8/10 of the CFHR5 gene, which is predicted to change the amino acid arginine at position 441 in the protein to cysteine. The variant is rare in population databases (gnomAD allele frequency = 0.0013%; 2 het and 0 hom in 152104 sequenced alleles; highest frequency = 0.0029%, Non-Finnish European population) (PM2). The variant has been reported in dbSNP (rs769456068) and in the HGMD database as possibly disease causing (CM2020115). It has not been reported in ClinVar. literature: PMID:33213850 - Variant listed as a VUS and was identified in a Korean adult patient with aHUS. |
Fulgent Genetics, |
RCV005012961 | SCV005635226 | uncertain significance | C3 glomerulonephritis | 2023-12-22 | criteria provided, single submitter | clinical testing |