Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001913880 | SCV002178118 | uncertain significance | Herpes simplex encephalitis, susceptibility to, 1 | 2021-09-09 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. This variant has not been reported in the literature in individuals with UNC93B1-related conditions. This variant is present in population databases (rs750569131, ExAC 0.007%). This sequence change replaces histidine with arginine at codon 191 of the UNC93B1 protein (p.His191Arg). The histidine residue is weakly conserved and there is a small physicochemical difference between histidine and arginine. |
Ambry Genetics | RCV004042848 | SCV004977934 | uncertain significance | not specified | 2024-02-05 | criteria provided, single submitter | clinical testing | The c.572A>G (p.H191R) alteration is located in exon 5 (coding exon 5) of the UNC93B1 gene. This alteration results from a A to G substitution at nucleotide position 572, causing the histidine (H) at amino acid position 191 to be replaced by an arginine (R). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |