Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Genetics Laboratory, |
RCV001172805 | SCV001335874 | uncertain significance | Charcot-Marie-Tooth disease | criteria provided, single submitter | clinical testing | ||
Ambry Genetics | RCV002393383 | SCV002668615 | uncertain significance | Inborn genetic diseases | 2022-03-24 | criteria provided, single submitter | clinical testing | The p.G415V variant (also known as c.1244G>T), located in coding exon 12 of the SBF2 gene, results from a G to T substitution at nucleotide position 1244. The glycine at codon 415 is replaced by valine, an amino acid with dissimilar properties. This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |