Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001045497 | SCV001209352 | pathogenic | Charcot-Marie-Tooth disease type 4 | 2019-11-27 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This sequence change creates a premature translational stop signal (p.Arg1196*) in the SBF2 gene. It is expected to result in an absent or disrupted protein product. This variant has been observed in individual(s) with Charcot-Marie-Tooth disease (PMID: 12687498). It has also been observed to segregate with disease in related individuals. ClinVar contains an entry for this variant (Variation ID: 2911). This variant is not present in population databases (ExAC no frequency). Loss-of-function variants in SBF2 are known to be pathogenic (PMID: 25873783, 12687498). |
OMIM | RCV004700181 | SCV000023203 | pathogenic | Charcot-Marie-Tooth disease type 4B2 | 2003-05-01 | no assertion criteria provided | literature only |