Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV001921045 | SCV002190757 | pathogenic | Cerebral cavernous malformation 2 | 2023-03-17 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals affected with CCM2-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change creates a premature translational stop signal (p.Leu177Cysfs*57) in the CCM2 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in CCM2 are known to be pathogenic (PMID: 18300272, 24689081). ClinVar contains an entry for this variant (Variation ID: 1415667). For these reasons, this variant has been classified as Pathogenic. |