Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Kasturba Medical College, |
RCV000211114 | SCV002562212 | likely pathogenic | Neurodegeneration with brain iron accumulation 4 | criteria provided, single submitter | clinical testing | ||
3billion, |
RCV000211114 | SCV002572595 | likely pathogenic | Neurodegeneration with brain iron accumulation 4 | 2022-09-01 | criteria provided, single submitter | clinical testing | The variant is observed at an extremely low frequency in the gnomAD v2.1.1 dataset (total allele frequency: 0.002%). In silico tool predictions suggest damaging effect of the variant on gene or gene product (REVEL: 0.84; 3Cnet: 0.74). Same nucleotide change resulting in same amino acid change has been previously reported as pathogenic/likely pathogenic with strong evidence (PMID: 26187298). The variant has been reported to co-segregate with the disease in at least one similarly affected relative/individual in the same family or similarly affected unrelated family (PMID: 26187298). Therefore, this variant is classified as Likely pathogenic according to the recommendation of ACMG/AMP guideline. |
OMIM | RCV000211114 | SCV000268062 | pathogenic | Neurodegeneration with brain iron accumulation 4 | 2013-01-15 | no assertion criteria provided | literature only |