Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000351851 | SCV000330801 | pathogenic | not provided | 2022-12-06 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss-of-function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 28815871) |
Genetics and Molecular Pathology, |
RCV002272203 | SCV002556802 | pathogenic | Developmental and epileptic encephalopathy, 54 | 2021-09-03 | criteria provided, single submitter | clinical testing | The HNRNPU c.520C>T variant is classified as PATHOGENIC (PVS1, PS2, PM2) The HNRNPU c.520C>T variant is a single nucleotide change which is predicted to result in premature termination of the protein product at codon 174 (PVS1). This variant is de novo in this individual (PS2). This variant is in dbSNP (rs886041983) but is absent from population databases (PM2). This variant has been reported in ClinVar as Pathogenic for an unnamed disorder by another diagnostic laboratory (Variation ID: 280850). |