Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002590497 | SCV002957623 | uncertain significance | not provided | 2022-08-07 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals affected with HMCN1-related conditions. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces histidine, which is basic and polar, with leucine, which is neutral and non-polar, at codon 4973 of the HMCN1 protein (p.His4973Leu). |
Ambry Genetics | RCV004065663 | SCV004090838 | uncertain significance | not specified | 2023-08-15 | criteria provided, single submitter | clinical testing | The c.14918A>T (p.H4973L) alteration is located in exon 96 (coding exon 96) of the HMCN1 gene. This alteration results from a A to T substitution at nucleotide position 14918, causing the histidine (H) at amino acid position 4973 to be replaced by a leucine (L). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Genome- |
RCV003456294 | SCV004180609 | uncertain significance | Age related macular degeneration 1 | 2023-04-11 | criteria provided, single submitter | clinical testing |