Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002770693 | SCV003025653 | uncertain significance | not provided | 2022-11-17 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. This variant has not been reported in the literature in individuals affected with HMCN1-related conditions. This variant is present in population databases (rs145955604, gnomAD 0.006%). This sequence change replaces methionine, which is neutral and non-polar, with threonine, which is neutral and polar, at codon 5314 of the HMCN1 protein (p.Met5314Thr). |
Ambry Genetics | RCV004064742 | SCV003594904 | uncertain significance | not specified | 2021-11-08 | criteria provided, single submitter | clinical testing | The c.15941T>C (p.M5314T) alteration is located in exon 103 (coding exon 103) of the HMCN1 gene. This alteration results from a T to C substitution at nucleotide position 15941, causing the methionine (M) at amino acid position 5314 to be replaced by a threonine (T). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Genome- |
RCV003456297 | SCV004180644 | uncertain significance | Age related macular degeneration 1 | 2023-04-11 | criteria provided, single submitter | clinical testing |