Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002041049 | SCV002316553 | uncertain significance | Familial cancer of breast; Fanconi anemia complementation group J | 2021-01-18 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (ExAC no frequency). This sequence change replaces arginine with glycine at codon 34 of the BRIP1 protein (p.Arg34Gly). The arginine residue is highly conserved and there is a moderate physicochemical difference between arginine and glycine. This variant has not been reported in the literature in individuals with BRIP1-related conditions. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Class C0"). |
Baylor Genetics | RCV003464395 | SCV004214747 | uncertain significance | Familial cancer of breast | 2023-09-20 | criteria provided, single submitter | clinical testing |