Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004517834 | SCV005029220 | pathogenic | Hereditary cancer-predisposing syndrome | 2023-12-04 | criteria provided, single submitter | clinical testing | The c.1483delT pathogenic mutation, located in coding exon 10 of the BRIP1 gene, results from a deletion of one nucleotide at nucleotide position 1483, causing a translational frameshift with a predicted alternate stop codon (p.S495Lfs*31). This variant is considered to be rare based on population cohorts in the Genome Aggregation Database (gnomAD). This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |