Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002399486 | SCV002713702 | pathogenic | Hereditary cancer-predisposing syndrome | 2022-06-23 | criteria provided, single submitter | clinical testing | The c.1727dupA pathogenic mutation, located in coding exon 11 of the BRIP1 gene, results from a duplication of A at nucleotide position 1727, causing a translational frameshift with a predicted alternate stop codon (p.N576Kfs*2). This variant was identified in a cohort of 681 ancestrally diverse, healthy subjects (Bodian DL et al. PLoS One, 2014 Apr;9:e94554). This variant is considered to be rare based on population cohorts in the Genome Aggregation Database (gnomAD). This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |
Myriad Genetics, |
RCV003335106 | SCV004044170 | pathogenic | Familial cancer of breast | 2023-06-05 | criteria provided, single submitter | clinical testing | This variant is considered pathogenic. This variant creates a frameshift predicted to result in premature protein truncation. |
ITMI | RCV000120390 | SCV000084542 | not provided | not specified | 2013-09-19 | no assertion provided | reference population |