Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001876263 | SCV002225807 | uncertain significance | Familial cancer of breast; Fanconi anemia complementation group J | 2021-10-02 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. ClinVar contains an entry for this variant (Variation ID: 929547). This missense change has been observed in individual(s) with prostate cancer (PMID: 31214711). This variant is present in population databases (rs765816425, ExAC 0.01%). This sequence change replaces asparagine with aspartic acid at codon 666 of the BRIP1 protein (p.Asn666Asp). The asparagine residue is weakly conserved and there is a small physicochemical difference between asparagine and aspartic acid. |
Ambry Genetics | RCV002418656 | SCV002718608 | uncertain significance | Hereditary cancer-predisposing syndrome | 2020-11-24 | criteria provided, single submitter | clinical testing | The p.N666D variant (also known as c.1996A>G), located in coding exon 13 of the BRIP1 gene, results from an A to G substitution at nucleotide position 1996. The asparagine at codon 666 is replaced by aspartic acid, an amino acid with highly similar properties. This amino acid position is poorly conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Leiden Open Variation Database | RCV001194764 | SCV001364547 | uncertain significance | not provided | 2019-08-13 | no assertion criteria provided | curation | Curator: Arleen D. Auerbach. Submitter to LOVD: Yukihide Momozawa. |