Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV001020907 | SCV001182451 | uncertain significance | Hereditary cancer-predisposing syndrome | 2019-09-11 | criteria provided, single submitter | clinical testing | The c.3699delC variant, located in coding exon 19 of the BRIP1 gene, results from a deletion of one nucleotide at nucleotide position 3699, causing a translational frameshift with a predicted alternate stop codon (p.F1234Lfs*20). Frameshifts are typically deleterious in nature, however, this frameshift occurs at the 3' terminus of BRIP1, is not expected to trigger nonsense-mediated mRNA decay, impacts only the last 16 amino acids of the protein, and results in the elongation of the protein by 3 amino acids. The exact functional impact of these altered/added amino acids is unknown at this time. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |